XLYS TYR Glutaridon (3x500g Tin)

Nutrition Facts - XLYS TRY Glutaridon

XLYS TRY Glutaridon is an unflavoured lysine and tryptophan-free powdered blend of essential and non-essential amino acids for the dietary management of glutaric aciduria type 1 (GA1). It is available in 500g tin format.

Macronutrients

Minerals

Amino Acid Profile

XLYS TRY Glutaridon contains a balanced blend of essential and non-essential amino acids specifically formulated to be free of lysine and tryptophan. The formula includes L-Leucine, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, L-Isoleucine, Glycine, L-Aspartic Acid, L-Threonine, L-Tyrosine, L-Phenylalanine, L-Serine, L-Alanine, L-Histidine, L-Cysteine, L-Methionine, and L-Glutamine.

Lysine & Tryptophan Content

Lysine: 0g (Lysine-Free) | Tryptophan: 0g (Tryptophan-Free)

Other Nutrient Information

Ingredients

XLYS TRY Glutaridon is a lysine and tryptophan-free powdered formula containing a balanced mix of amino acids and carbohydrate.

L-Leucine, L-Glutamic Acid, L-Proline, L-Arginine, L-Valine, L-Isoleucine, Glycine, L-Aspartic Acid, L-Threonine, L-Tyrosine, L-Phenylalanine, L-Serine, Dried Glucose Syrup, L-Alanine, L-Histidine, L-Cysteine, L-Methionine, L-Glutamine, Tricalcium Phosphate, Taurine, L-Carnitine.

Allergy Advice

For allergens, see ingredients in bold. No major allergens declared.

Important Notice

Suitability

Vegetarian

Preparation and Directions for Usage

XLYS TRY Glutaridon is a powdered supplement that requires preparation. The quantity of feed and dilution should be determined by a clinician or dietitian only, and is dependent on the age, body weight and medical condition of the patient.

Preparation Instructions

The recommended dosage and timing of intake is dependent on the age, bodyweight and medical condition of the patient, and should be determined by a dietitian or clinician only. The recommended dilution is 1 to 20 (i.e. 5g of XLYS TRY Glutaridon plus 100mls of water). To prepare, add a small amount of Glutaridon and stir with a fork until a smooth paste is obtained. Continue stirring whilst adding the remaining volume of water. Glutaridon can be taken as a chilled drink. It can also be taken as a paste, additional water or diluted drinks must be consumed at the same time. Glutaridon may be also flavoured with a separate flavour from the Nutricia flavour range. Please note flavouring is not recommended for infants less than six months.

Scoop Information

Scoop Weight: 1 level scoop provides 37.5g of powder

Dosage Information

The dosage is clinician/dietitian determined and is dependent on the age, body weight and medical condition of the patient.

Storage & Shelf Life

Storage: Store in a cool dry place. Always replace the container lid after use. Once opened, use within one month.

Shelf Life: 24 months

Product Information

Format: Powdered Amino Acid Formula | Pack Size: 500g Tin | Flavour: Unflavoured | Scoop Weight: 37.5g per level scoop

Medical Supervision

This product must be used under medical supervision. Not intended as sole source of nutrition. Use only as a supplement under professional guidance. Suitable from birth for glutaric aciduria type 1 (GA1) management.

Special Considerations

Lysine & Tryptophan-Free: XLYS TRY Glutaridon is specifically formulated to be completely free of lysine and tryptophan, making it suitable for glutaric aciduria type 1 (GA1) management.

Balanced Amino Acid Formula: The formula contains a balanced mix of essential and non-essential amino acids to support overall nutrition while avoiding lysine and tryptophan.

Suitable from Birth: XLYS TRY Glutaridon is suitable for use from birth for infants and children with proven glutaric aciduria type 1 (GA1).

Must Be Supplemented: This product is not suitable as a sole source of nutrition and must be supplemented with a natural protein source to provide lysine, tryptophan, and other essential nutrients as prescribed by a clinician or dietitian.

Flavouring Options: XLYS TRY Glutaridon may be flavoured with a separate flavouring from the Nutricia flavour range to improve palatability. Flavouring is not recommended for infants less than six months.

Osmolality Consideration: The product can be taken as a more concentrated drink or paste, however water or diluted drinks should also be taken to counteract high osmolality (360 mOsmol/kg H2O at 1:20 dilution).

Metabolic Disorder Specific: Specifically designed for glutaric aciduria type 1 (GA1) management. Not suitable for other metabolic disorders.