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View compareSpecialized Medical Formula: Unflavoured phenylalanine and tyrosine-free powdered blend of essential and non-essential amino acids for dietary management of proven tyrosinaemia where plasma methionine levels are normal. Must be supplemented with natural protein source. Suitable from birth. Requires vitamins, minerals and trace elements supplement (e.g. Phlexy-Vits).
Medical Benefits
Nutrition Facts - XPHEN TYR Tyrosidon
XPHEN TYR Tyrosidon is an unflavoured phenylalanine and tyrosine-free powdered blend of essential and non-essential amino acids for the dietary management of proven tyrosinaemia where plasma methionine levels are normal. It is available in 500g tin format.
Macronutrients
| Nutrient | Unit | Per 100g | Per 5g |
|---|---|---|---|
| Energy | kcal | 326 | 16.3 |
| Energy | kJ | 1386 | 69.3 |
| Protein | g | 77 | 3.9 |
| Carbohydrate | g | 4.5 | 0.23 |
| - Sugars | g | 0.4 | 0.02 |
| - Lactose | g | 0 | 0 |
| Fat | g | 0 | 0 |
| Fibre | g | 0 | 0 |
Minerals
| Nutrient | Unit | Per 100g | Per 5g |
|---|---|---|---|
| Sodium | mg (mmol) | <20 (<0.9) | <1 (<0.05) |
| Calcium | mg (mmol) | 126 (3.1) | 6.3 (0.15) |
| Phosphorus | mg (mmol) | 65 (2.1) | 3.25 (0.1) |
Amino Acid Profile
| Amino Acid | Unit | Per 100g | Per 5g |
|---|---|---|---|
| L-Alanine | g | 4.1 | 0.21 |
| L-Arginine | g | 7.16 | 0.36 |
| L-Aspartic Acid | g | 5.98 | 0.3 |
| L-Cysteine | g | 2.66 | 0.13 |
| Glycine | g | 6.4 | 0.32 |
| L-Glutamine | g | 0.81 | 0.04 |
| L-Histidine | g | 4.09 | 0.2 |
| L-Isoleucine | g | 6.4 | 0.32 |
| L-Leucine | g | 10.97 | 0.55 |
| L-Lysine | g | 7.46 | 0.37 |
| L-Methionine | g | 1.75 | 0.09 |
| L-Phenylalanine | g | 0 | 0 |
| L-Proline | g | 7.77 | 0.39 |
| L-Serine | g | 4.79 | 0.24 |
| L-Threonine | g | 5.38 | 0.27 |
| L-Tryptophan | g | 2.15 | 0.11 |
| L-Tyrosine | g | 0 | 0 |
| L-Valine | g | 6.99 | 0.35 |
| L-Carnitine | g | 0.06 | 0.003 |
| Taurine | g | 0.12 | 0.006 |
Other Nutrient Information
| Nutrient | Unit | Per 5g (1:20 dilution) |
|---|---|---|
| Osmolality | mOsmol/kg H2O | 370 |
Ingredients
XPHEN TYR Tyrosidon is a phenylalanine and tyrosine-free powdered formula containing a balanced mix of amino acids and carbohydrate.
L-Lysine L-Glutamate, L-Leucine, L-Proline, L-Arginine, L-Valine, L-Isoleucine, Glycine, L-Aspartic Acid, L-Threonine, L-Serine, Dried Glucose Syrup, L-Alanine, Histidine, L-Cysteine, L-Tryptophan, L-Methionine, L-Glutamine, L-Glutamic Acid, Tricalcium Phosphate, Taurine, L-Carnitine.
Allergy Advice
For allergens, see ingredients in bold. No major allergens declared.
Important Notice
Precautions
Must be used under medical supervision. For enteral use only. Not suitable for use as a sole source of nutrition. This product should not be used as a sole source of protein but must be given in conjunction with a protein source to supply the phenylalanine, tyrosine, fluid and general nutrition requirements of the patient in quantities as prescribed by a clinician or dietitian. For use from birth. For the dietary management of proven tyrosinaemia where plasma methionine levels are normal. A source of vitamins, minerals and trace elements is required (e.g. Phlexy-Vits).
Suitability
Vegetarian
Preparation and Directions for Usage
XPHEN TYR Tyrosidon is a powdered supplement that requires preparation. The quantity of feed and dilution should be determined by a clinician or dietitian only, and is dependent on the age, body weight and medical condition of the patient.
Preparation Instructions
The recommended dosage and timing of intake is dependent on the age, bodyweight and medical condition of the patient, and should be determined by a dietitian or clinician only. The recommended dilution is 1 to 20 (i.e. 5g of XPHEN TYR Tyrosidon plus 100mls of water). To prepare, add a small amount of Tyrosidon and stir with a fork until a smooth paste is obtained. Continue stirring whilst adding the remaining volume of water. Tyrosidon can be taken as a chilled drink. It can also be taken as a paste, additional water or diluted drinks must be consumed at the same time. Tyrosidon may be also flavoured with a separate flavour from the Nutricia flavour range. Please note flavouring is not recommended for infants less than six months.
Dosage Information
The dosage is clinician/dietitian determined and is dependent on the age, body weight and medical condition of the patient.
Storage & Shelf Life
Storage: Store in a cool dry place. Always replace the container lid after use. Once opened, use within one month. The prepared feed must be refrigerated and must not be kept longer than 24 hours.
Shelf Life: 24 months
Product Information
Format: Powdered Amino Acid Formula | Pack Size: 500g Tin | Flavour: Unflavoured | Dilution Ratio: 1:20 (5g powder + 100ml water)
Medical Supervision
This product must be used under medical supervision. Not intended as sole source of nutrition. Use only as a supplement under professional guidance. Suitable from birth for tyrosinaemia management where plasma methionine levels are normal.
Special Considerations
Phenylalanine & Tyrosine-Free: XPHEN TYR Tyrosidon is specifically formulated to be completely free of phenylalanine and tyrosine, making it suitable for tyrosinaemia management where plasma methionine levels are normal.
Balanced Amino Acid Formula: The formula contains a balanced mix of essential and non-essential amino acids to support overall nutrition while avoiding phenylalanine and tyrosine.
Suitable from Birth: XPHEN TYR Tyrosidon is suitable for use from birth for infants and children with proven tyrosinaemia where plasma methionine levels are normal.
Must Be Supplemented: This product is not suitable as a sole source of nutrition and must be supplemented with a natural protein source to provide phenylalanine, tyrosine, and other essential nutrients as prescribed by a clinician or dietitian.
Vitamin & Mineral Supplementation Required: A source of vitamins, minerals and trace elements is required (e.g. Phlexy-Vits) to ensure complete nutritional support.
Preparation Method: Product requires careful preparation with water. Recommended dilution is 1:20 (5g powder + 100ml water). Can be taken as a chilled drink, paste, or diluted form. Prepared feed must be refrigerated and cannot be kept longer than 24 hours.
Flavouring Options: XPHEN TYR Tyrosidon may be flavoured with a separate flavouring from the Nutricia flavour range to improve palatability. Flavouring is not recommended for infants less than six months.
Osmolality Consideration: The product can be taken as a more concentrated drink or paste, however water or diluted drinks should also be taken to counteract high osmolality (370 mOsmol/kg H2O at 1:20 dilution).
Metabolic Disorder Specific: Specifically designed for tyrosinaemia management where plasma methionine levels are normal. Not suitable for other metabolic disorders or for patients with elevated plasma methionine levels.
Refrigeration Required: Prepared XPHEN TYR Tyrosidon feed must be refrigerated and cannot be kept longer than 24 hours after preparation.


