Nutri-sip
MSUD AID III (500g)
Description
Indication: Food for Special Medical Purposes for the dietary management of Maple Syrup Urine Disease (MSUD) in children 10 years and over and adults. An unflavoured isoleucine, leucine and valine-free powder, containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat, vitamins, minerals and trace elements.
Allergen Information
Nutrition Facts - MSUD Aid III per 100g
Macronutrients
| Nutrient | per 100g |
|---|---|
| Energy | 390 kcal (1635 kJ) |
| Protein | 40g |
| Carbohydrates | 30g |
| - Sugars | <1g |
| Fat | 15g |
| - Saturated Fat | 3g |
| - Monounsaturates | 8g |
| - Polyunsaturates | 3g |
| Fibre | 0g |
Vitamins (per 100g)
| Nutrient | per 100g |
|---|---|
| Vitamin A | 600μg |
| Vitamin D | 10μg |
| Vitamin E | 10mg (α-TE) |
| Vitamin K | 20μg |
| Thiamin | 1mg |
| Riboflavin | 1.2mg |
| Niacin | 10mg (NE) |
| Pantothenic Acid | 5mg |
| Vitamin B6 | 1.2mg |
| Folic Acid | 200μg |
| Vitamin B12 | 2μg |
| Biotin | 50μg |
| Vitamin C | 80mg |
Minerals (per 100g)
| Nutrient | per 100g |
|---|---|
| Sodium | 400mg (17.4 mmol) |
| Potassium | 1000mg (25.6 mmol) |
| Chloride | 600mg (16.9 mmol) |
| Calcium | 800mg (20 mmol) |
| Phosphorus | 600mg (19.4 mmol) |
| Magnesium | 200mg (8.2 mmol) |
| Iron | 15mg |
| Zinc | 10mg |
| Copper | 1mg |
| Manganese | 2mg |
| Molybdenum | 50μg |
| Selenium | 50μg |
| Chromium | 50μg |
| Iodine | 150μg |
Amino Acids (per 100g)
| Nutrient | per 100g |
|---|---|
| L-Alanine | 2g |
| L-Arginine | 2.5g |
| L-Aspartic Acid | 2g |
| L-Cystine | 1.5g |
| Glycine | 2.5g |
| L-Glutamine | 3g |
| L-Histidine | 1.5g |
| L-Isoleucine | 0g |
| L-Leucine | 0g |
| L-Lysine | 2.5g |
| L-Methionine | 0.5g |
| L-Phenylalanine | 1.5g |
| L-Proline | 3g |
| L-Serine | 2g |
| L-Threonine | 1.5g |
| L-Tryptophan | 0.5g |
| L-Tyrosine | 2.5g |
| L-Valine | 0g |
| L-Carnitine | 0.1g |
| Taurine | 0.5g |
Ingredients - MSUD Aid III
Product Description
MSUD Aid III is a Food for Special Medical Purposes for use under medical supervision. MSUD Aid III is an unflavoured isoleucine, leucine and valine-free powder, containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. For the dietary management of proven Maple Syrup Urine Disease in children 10 years and over and adults. The formula must be used as part of a comprehensive dietary management plan and given in conjunction with a protein source to supply the leucine, isoleucine, valine, fluid and general nutrition requirements as prescribed by a clinician or dietitian.
Ingredients List
Dried glucose syrup, L-alanine, L-arginine, glycine, L-glutamine, L-lysine hydrochloride, L-proline, L-serine, L-threonine, L-tyrosine, L-cystine, L-histidine, L-methionine, L-phenylalanine, L-tryptophan, L-aspartic acid, taurine, L-carnitine, refined vegetable oils (high oleic sunflower oil, canola oil, medium chain triglycerides), calcium phosphate dibasic, potassium chloride, magnesium oxide, sodium chloride, ferrous sulphate, zinc sulphate, copper sulphate, manganese sulphate, potassium iodide, sodium molybdate, sodium selenite, chromium chloride, vitamin A acetate, cholecalciferol (vitamin D3), DL-α tocopheryl acetate, phylloquinone (vitamin K1), thiamine hydrochloride, riboflavin, nicotinamide, D-pantothenic acid (calcium salt), pyridoxine hydrochloride, cyanocobalamin, folic acid, D-biotin, L-ascorbic acid, choline bitartrate, inositol.
Allergy Advice: Gluten free, lactose free. For allergens, see ingredients in bold.
Usage & Administration - MSUD Aid III
Indications
For the dietary management of Maple Syrup Urine Disease (MSUD) in children 10 years and over and adults. ACBS approved, prescribable on form FP10 (GP10 in Scotland).
Contra-Indications
Not suitable for children under 10 years. Not suitable for use as a sole source of nutrition. This product should not be used as a sole source of protein but must be given in conjunction with a protein source to supply the leucine, isoleucine, valine, fluid and general nutrition requirements of the patient in quantities as prescribed by a clinician or dietitian.
Precautions
Must be used under medical supervision. For enteral use only. Regular monitoring of plasma amino acid levels is essential. Adequate fluid intake must be maintained.
Preparation and Directions for Use
The recommended dosage is dependent on the age, bodyweight and medical condition of the patient, and should be determined by a clinician or dietitian only. Mix the powder with water or permitted drinks as directed by the dietitian. The typical reconstitution is 1 part powder to 3 parts water by weight to give a 25% solution (approximately 1.03 kcal/ml).
Storage
Store in a cool, dry place away from sunlight. Once reconstituted, keep refrigerated and use within 24 hours.
Shelf Life
As indicated on the packaging.
Manufacturer Details
Product: MSUD Aid III 500g Tin
Order Code: 116177
PIP Code: 211-9202
Manufactured by: Nutricia, a Danone Company
