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View compareGA1 Management: GA amino5 is an unflavoured powdered lysine and tryptophan-free protein substitute containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. For use in dietary management of Glutaric Aciduria Type 1 from birth onwards.
Nutritional Information
Nutrition Facts - GA amino5
Each 6g sachet provides 5g protein equivalent and complete nutritional support for Glutaric Aciduria Type 1 management. Lysine is completely absent.
Macronutrients per 6g Sachet
| Nutrient | Per 100g | Per 6g Sachet |
|---|---|---|
| Energy (kJ) | 1411 | 85 |
| Energy (kcal) | 332 | 20 |
| Fat (g) | 0 | 0 |
| Carbohydrate (g) | 0 | 0 |
| Protein (equivalent) (g) | 83 | 5 |
| L-Lysine (g) | 0 | 0 |
| L-Tryptophan (g) | 0.63 | 0.04 |
| Salt (g) | 0 | 0 |
Amino Acids per 6g Sachet
| Amino Acid | Per 100g (g) | Per 6g Sachet (g) |
|---|---|---|
| L-Alanine | 8.95 | 0.54 |
| L-Arginine | 8.39 | 0.50 |
| L-Aspartic Acid | 5.23 | 0.31 |
| L-Cystine | 3.20 | 0.19 |
| L-Glutamine | 5.23 | 0.31 |
| Glycine | 4.53 | 0.27 |
| L-Histidine | 3.52 | 0.21 |
| L-Isoleucine | 7.25 | 0.44 |
| L-Leucine | 12.58 | 0.75 |
| L-Methionine | 2.21 | 0.13 |
| L-Ornithine | 0.00 | 0.00 |
| L-Phenylalanine | 6.04 | 0.36 |
| L-Proline | 7.05 | 0.42 |
| L-Serine | 5.54 | 0.33 |
| L-Threonine | 6.04 | 0.36 |
| L-Tyrosine | 7.05 | 0.42 |
| L-Valine | 8.05 | 0.48 |
| L-Carnitine | 0.00 mg | 0.00 mg |
| Taurine | 0.00 mg | 0.00 mg |
Ingredients & Warnings
GA amino5 contains amino acids. Lysine is completely absent and tryptophan is minimal (0.04g per sachet).
Important Warnings & Precautions
- Must only be given to individuals with proven Glutaric Aciduria Type 1 under strict medical supervision
- Suitable from birth onwards
- Diet must be supplemented with natural protein, water and other nutrients in prescribed quantities to supply lysine, tryptophan, fluid and general nutritional requirements
- Not for use as a sole source of nutrition
- For enteral use only
- Unflavoured
- Keep out of reach of children
Storage Instructions
- Store in a cool, dry place
- Sachets are designed for single use and should be used immediately after opening
- Any unused powder in an open sachet must be tightly sealed and used within 24 hours
Preparation Instructions
- The product should be freshly prepared and consumed immediately
- If this is not possible, all prepared product must be tightly covered and consumed within 4 hours if kept at room temperature, or within 24 hours if refrigerated
- Shake before use
Usage & Storage
Dosage and Administration
To be determined by the clinician or dietitian and is dependent on the age, body weight and medical condition of the patient.
GA amino5 (6g) = 5g Protein Equivalent (PE)
Preparation Guidelines
GA amino5 can be used in the dietary management of GA1 in a variety of ways:
- Mixed in with protein substitute
- Added to modular feeds
- Incorporated into other permitted food or drink
For Bottle Fed Infants:
- Sterilise feeding equipment according to manufacturer's instructions
- Follow the feed preparation instructions provided by your dietitian or clinician
- Use immediately and discard any remaining product after 1 hour
- Do not reheat once feeding has started
Important Usage Notes
- Ideally the product should be freshly prepared and used immediately
- If this is not possible, all prepared product must be tightly covered and consumed within 4 hours if kept at room temperature, or within 24 hours if refrigerated
- Shake before use
Storage Instructions
- Store in a cool, dry place
- Keep away from direct sunlight and moisture
- Keep container tightly closed
- Sachets are designed for single use and should be used immediately after opening
- Any unused powder should be tightly sealed and used within 24 hours
Medical Supervision
GA amino5 must only be given to individuals with proven Glutaric Aciduria Type 1 under strict medical supervision. Regular monitoring of plasma amino acids is essential to ensure appropriate management and prevent metabolic complications.
Indications
For use in the dietary management of Glutaric Aciduria Type 1 (GA1) from birth onwards. Must be supplemented with natural protein source to provide lysine, tryptophan and other essential nutrients.

